{"_buckets": {"deposit": "e1f4abf7-831c-4f80-bfeb-b27f2dc04b02"}, "_deposit": {"created_by": 19, "id": "11432", "owners": [19], "pid": {"revision_id": 0, "type": "depid", "value": "11432"}, "status": "published"}, "_oai": {"id": "oai:asahi-u.repo.nii.ac.jp:00011432", "sets": ["123"]}, "author_link": ["14642"], "item_10_creator_30": {"attribute_name": "教員氏名", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "宮﨑, 渚"}], "nameIdentifiers": [{"nameIdentifier": "14642", "nameIdentifierScheme": "WEKO"}]}]}, "item_10_date_36": {"attribute_name": "発行又は発表の年月", "attribute_value_mlt": [{"subitem_date_issued_datetime": "2019-09"}]}, "item_10_textarea_29": {"attribute_name": "業績分類", "attribute_value_mlt": [{"subitem_textarea_value": "学術雑誌論文"}]}, "item_10_textarea_31": {"attribute_name": "発行、発表雑誌等、又は発表学会等の名称", "attribute_value_mlt": [{"subitem_textarea_value": "Circulation Journal"}]}, "item_10_textarea_32": {"attribute_name": "巻", "attribute_value_mlt": [{"subitem_textarea_value": "83"}]}, "item_10_textarea_33": {"attribute_name": "号", "attribute_value_mlt": [{"subitem_textarea_value": "10"}]}, "item_10_textarea_34": {"attribute_name": "掲載ページ", "attribute_value_mlt": [{"subitem_textarea_value": "2081"}]}, "item_10_textarea_35": {"attribute_name": "単著、共著の別", "attribute_value_mlt": [{"subitem_textarea_value": "共著"}]}, "item_10_textarea_42": {"attribute_name": "概要", "attribute_value_mlt": [{"subitem_textarea_value": "ファブリー病における酵素補充療法の前後で電顕で組織の評価ができた3例（2例は生検、1例は剖検）について、酵素補充療法後ではミエリン体が不鮮明になり、電子の抜けた部分が増えている様子が観察され、酵素補充療法の効果と考えられた。"}]}, "item_access_right": {"attribute_name": "アクセス権", "attribute_value_mlt": [{"subitem_access_right": "metadata only access", "subitem_access_right_uri": "http://purl.org/coar/access_right/c_14cb"}]}, "item_language": {"attribute_name": "言語", "attribute_value_mlt": [{"subitem_language": "eng"}]}, "item_resource_type": {"attribute_name": "資源タイプ", "attribute_value_mlt": [{"resourcetype": "other", "resourceuri": "http://purl.org/coar/resource_type/c_1843"}]}, "item_title": "Ultrastructural Evidence of Glycosphingolipid Degradation After Enzyme Replacement Therapy in Patients With Fabry Disease.", "item_titles": {"attribute_name": "タイトル", "attribute_value_mlt": [{"subitem_title": "Ultrastructural Evidence of Glycosphingolipid Degradation After Enzyme Replacement Therapy in Patients With Fabry Disease."}]}, "item_type_id": "10", "owner": "19", "path": ["123"], "permalink_uri": "https://asahi-u.repo.nii.ac.jp/records/11432", "pubdate": {"attribute_name": "公開日", "attribute_value": "2019-11-21"}, "publish_date": "2019-11-21", "publish_status": "0", "recid": "11432", "relation": {}, "relation_version_is_last": true, "title": ["Ultrastructural Evidence of Glycosphingolipid Degradation After Enzyme Replacement Therapy in Patients With Fabry Disease."], "weko_shared_id": -1}